Hemin

He aha te Hemin?

He rongoā te Hemin i ahu mai i te heme, te wāhanga rino o te hemoglobin e kitea ana i roto i ngā toto whero. Ko te nuinga o te wā ka whakamahia hei rongoā i te porphyria whakapeka, he rōpū mate ira onge e pā ana ki te hanga heme. Ka āwhina te Hemin ki te whakamama i ngā tohu e pā ana ki ngā whakaekenga porphyria mā te whakarato i te tinana ki te puna heme, ā, ka whakaiti i te hanga o ngā porphyrin ka taea te kohikohi me te whakaputa i ngā raruraru hauora.

Ngā Whakamahinga o Hemin

Kua whakaaetia a Hemin mō te rongoā i ngā whakaekenga ohorere o te porphyria, inā koa ko te porphyria wā-poto (AIP). He whai hua ki te whakahaere i ngā tohu pēnei i te mamae nui o te puku, ngā raruraru pūnaha io, me ētahi atu āhuatanga o te mate. Mā te whakarato i te heme, ka āwhina a Hemin ki te whakahoki i te taurite o te hanga heme, ā, ka ārai i ngā raruraru anō.

Kia pehea te Works te reira

Ka mahi a Hemin mā te whakarato i te heme ki te tinana, he mea nui mō ngā tukanga koiora maha. Mō ngā tāngata whai porphyria, kāore e taea e te tinana te whakaputa i te heme nui nā te ngoikore o ngā whākōkī. Mā te tuku i a Hemin, ka whiwhi te tinana i te heme o waho, e pehi ana i te ate delta-aminolevulinic acid (ALA) synthase, ā, nā reira ka whakaitihia te whakaputanga nui o ngā matū porphyrin. Ka āwhina tēnei mahi ki te whakamamae i ngā tohu o ngā whakaekenga porphyria me te ārai i ngā raruraru anō.

Te Inenga me te Whakahaerenga

Ka rerekē te horopeta paerewa o Hemin i runga i te kaha o te mate me te urupare a te tūroro. Mō ngā pakeke, ko te horopeta tuatahi he 3 ki te 4 mg/kg e tukuna ana mā te uaua, ā, muri iho ka tāpirihia ngā horopeta ina hiahiatia. Ka whakatauhia ngā horopeta tamariki i runga i te taumaha me te āhua haumanu o te tamaiti. I te nuinga o te wā ka hoatu a Hemin i roto i te hōhipera i raro i te tirotiro a te rata hei aroturuki i ngā pānga kino.

Ngā Pānga Taha o Hemin

Ko ngā pānga taha noa o Hemin ko:

• whakapairuaki
• Te mate
• Mamae mamae
• He kirika
• Fever

Ka taea e nga paanga kino te whakauru:

• Nga tauhohenga mate pāwera (te ponana, te patito, te pupuhi)
• Thrombosis (whakaheke toto)
• Te tauritenga hiko
• Te nui rawa o te rino (mēnā ka whakamahia tonutia)
• Te phlebitis i te wāhi werohanga

Me whakaatu wawe nga turoro i nga tohu rereke ki o raatau ratonga hauora.

Ngä Whakauru Iwi

Ka taunekeneke pea a Hemin me ētahi rongoā, tae atu ki:

• Anticoagulants (whakaongoi toto)
• Ko etahi atu rongoa ka pa ki nga enzyme ate
• Ko ētahi paturopi, inā koa ko ērā e whakaoho ana i ngā whākōkī ate

He mea nui ki te whakamohio ki to kaiwhakarato hauora mo nga rongoa me nga taapiri katoa e tangohia ana e koe hei karo i nga taunekeneke pea.

Nga painga o Hemin

Ko te painga matua o Hemin ko tōna kaha ki te whakahaere tika i ngā whakaekenga porphyria whakapeka, e whakarato ana i te whakaora tere i ngā tohu ngoikore. Hei tāpiri, ka āwhina i te aukati i ngā whakaekenga a meake nei mā te whakahoki mai i te taurite heme i roto i te tinana. He kōwhiringa maimoatanga nui a Hemin mō te hunga whai porphyria, e whakapai ake ana i te kounga o ō rātou oranga.

Ngā Contraindications mō te whakamahi i a Hemin

Me karohia te Hemin mō te hunga whai:

• Te mōhiotia he pāwera ki te heme, ki tētahi wāhanga rānei o te hanganga
• Te mate ate tino
• Te toto toto kaha

Me kōrero ngā wāhine hapū, ngā wāhine whāngai u rānei ki tā rātou kaiwhakarato hauora i mua i te whakamahi i a Hemin, nā te mea kāore anō kia tino whakapūmautia tōna haumaru mō ēnei rōpū tāngata.

Whakatupato me nga Whakatupato

I mua atu, ā, i te wā e rongoatia ana ki a Hemin, me tirotirohia ngā tūroro i roto i te taiwhanga, tae atu ki ngā whakamātautau mahi ate, ngā tawhā toto totoka, me ngā taumata rino, hei aromatawai i ngā raruraru pea. He mea nui te whakamahi i a Hemin i raro i te tirotiro a tētahi tohunga hauora, inā koa mō ngā tūroro kua pāngia e ngā mate hauora o mua.

FAQs

He aha te whakamahinga o Hemin?

Ka whakamahia a Hemin hei rongoā i ngā whakaekenga whakapeka o te porphyria, inā koa ko te porphyria whakapeka whakapeka.

Me pēhea te hoatutanga o Hemin?

Ko te tikanga ka tukuna a Hemin mā roto i te uaua i roto i te hōhipera.

He aha ngā pānga taha e pā ana ki a Hemin?

Ko ngā pānga taha noa ko te whakapairuaki, te ruaki, te mamae o te puku, me te ānini.

Ka taea te whakamahi i te Hemin mō ngā tamariki?

Ae, ka taea te whakamahi i a Hemin mō ngā tamariki, engari ka whakarerekētia te horopeta i runga i te taumaha me te āhua haumanu.

He nui nga paanga kino?

Ae, ko ngā pānga taha kino ka uru atu ki ngā mate pāwera me ngā toto totoka.

Me aha ahau ki te ngaro ahau i te horopeta?

Mena ka ngaro koe i te horopeta, whakapaa atu ki to kaiwhakarato hauora mo te arahi mo nga mahi ka whai ake.

Ka taea e Hemin te taunekeneke me ētahi atu rongoā?

Ae, ka taea e Hemin te taunekeneke me ngā rongoā ārai toto me ētahi atu rongoā e pā ana ki ngā whākōkī ate.

He haumaru te whakamahi i a Hemin i te wā e hapu ana?

Kāore anō kia tino whakapumautia te haumaru o te tango i te Hemin i te wā e hapu ana; me toro atu ki tō tākuta.

Me pēhea te mahi a Hemin?

Ka whakaratohia e Hemin te heme ki te tinana, ka āwhina i te whakaiti i te hanga o ngā porphyrin i roto i te porphyria.

Kei hea ahau e whiwhi ai i a Hemin?

Kei te wātea a Hemin mā te whakahaunga a te taote, ā, i te nuinga o te wā ka tukuna i roto i te hōhipera, i te wāhi haumanu rānei.

Nga Ingoa Tohu

Kei te hokohokohia a Hemin i raro i ngā ingoa waitohu maha, tae atu ki a Panhematin.

Opaniraa

He mea nui te mahi a te Hemin i roto i te whakahaere i te porphyria whakapeka, e whakarato ana i te heme nui hei whakamama i ngā tohu me te ārai i ngā whakaekenga a meake nei. Nā tōna whai huatanga me tōna kaha ki te whakapai ake i te kounga o te oranga mō te hunga whai porphyria, he mea nui tēnei hei rongoā i roto i te ao maimoatanga. Me kōrero tonu ki tētahi kaiwhakarato hauora mō ngā tohutohu whaiaro me ngā kōwhiringa maimoatanga.